Congenital cystic adenomatoid malformation of lung: Report of two cases with review of literature

Lung India. 2013 Jul;30(3):215-8. doi: 10.4103/0970-2113.116272.

Abstract

Congenital cystic adenomatoid malformations (CCAM) also known as congenital pulmonary airway malformation is a developmental, non-hereditary, hamartomatous abnormality of lung with unknown etiology. It is a rare disease with an incidence of 1 in 25,000 to 1 in 35,000. It is a disease of infancy with most of the cases diagnosed within first 2 years of life. We report autopsy findings of two fetuses with congenital cystic adenomatoid malformation (Stocker Type II and I) with brief review of literature.

Keywords: Congenital cystic adenomatoid malformation; fetal autopsy; lung.